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Escalating protein supersaturation underlies inclusion formation in muscle proteinopathies
Prajwal Ciryam, Matthew Antalek, Fernando Cid, Gian Gaetano Tartaglia, Christopher M. Dobson, Anne-Katrin Guttsches, Britta Eggers, Matthias Vorgerd, Katrin Marcus, Rudolf A. Kley, Richard I. Morimoto, Michele Vendruscolo, Conrad Weihl
doi: https://doi.org/10.1101/762245
Prajwal Ciryam
1Department of Neurology, Vagelos College of Physicians & Surgeons, Columbia University, New York NY
Matthew Antalek
2Rice Institute for Biomedical Research, Department of Molecular Biosciences, Northwestern University, Evanston IL
Fernando Cid
3Centre for Genomic Regulation, The Barcelona Institute of Science and Technology, Barcelona, Spain
Gian Gaetano Tartaglia
3Centre for Genomic Regulation, The Barcelona Institute of Science and Technology, Barcelona, Spain
Christopher M. Dobson
4Centre for Misfolding Diseases, Department of Chemistry, University of Cambridge, Cambridge UK
Anne-Katrin Guttsches
5Department of Neurology, Heimer Institute of Muscle Research, University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany
Britta Eggers
6Medizinisches Proteom-Center, Ruhr-University Bochum, Bochum, Germany
Matthias Vorgerd
5Department of Neurology, Heimer Institute of Muscle Research, University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany
Katrin Marcus
6Medizinisches Proteom-Center, Ruhr-University Bochum, Bochum, Germany
Rudolf A. Kley
7Department of Neurology, St. Marien Hospital Borken, University of Witten/Herdecke, Borken, Germany
Richard I. Morimoto
2Rice Institute for Biomedical Research, Department of Molecular Biosciences, Northwestern University, Evanston IL
Michele Vendruscolo
4Centre for Misfolding Diseases, Department of Chemistry, University of Cambridge, Cambridge UK
Conrad Weihl
8Department of Neurology and Hope Center for Neurological Disease, Washington University School of Medicine, Saint Louis MO
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Posted September 12, 2019.
Escalating protein supersaturation underlies inclusion formation in muscle proteinopathies
Prajwal Ciryam, Matthew Antalek, Fernando Cid, Gian Gaetano Tartaglia, Christopher M. Dobson, Anne-Katrin Guttsches, Britta Eggers, Matthias Vorgerd, Katrin Marcus, Rudolf A. Kley, Richard I. Morimoto, Michele Vendruscolo, Conrad Weihl
bioRxiv 762245; doi: https://doi.org/10.1101/762245
Escalating protein supersaturation underlies inclusion formation in muscle proteinopathies
Prajwal Ciryam, Matthew Antalek, Fernando Cid, Gian Gaetano Tartaglia, Christopher M. Dobson, Anne-Katrin Guttsches, Britta Eggers, Matthias Vorgerd, Katrin Marcus, Rudolf A. Kley, Richard I. Morimoto, Michele Vendruscolo, Conrad Weihl
bioRxiv 762245; doi: https://doi.org/10.1101/762245
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