Inborn errors of type I IFN immunity in patients with life-threatening COVID-19

…, JD Milner, DC Vinh, TH Mogensen, N Marr… - Science, 2020 - science.org
INTRODUCTION Clinical outcomes of human severe acute respiratory syndrome coronavirus
2 (SARS-CoV-2) infection range from silent infection to lethal coronavirus disease 2019 (…

X-linked recessive TLR7 deficiency in~ 1% of men under 60 years old with life-threatening COVID-19

…, H Abolhassani, S Mane, N Marr… - Science …, 2021 - science.org
Autosomal inborn errors of type I IFN immunity and autoantibodies against these cytokines
underlie at least 10% of critical COVID-19 pneumonia cases. We report very rare, …

Human IL-23 is essential for IFN-γ–dependent immunity to mycobacteria

…, B Boisson, C Fieschi, D Mansouri, N Marr… - Science …, 2023 - science.org
Patients with autosomal recessive (AR) IL-12p40 or IL-12Rβ1 deficiency display Mendelian
susceptibility to mycobacterial disease (MSMD) due to impaired IFN-γ production and, less …

Inherited PD-1 deficiency underlies tuberculosis and autoimmunity in a child

…, RP Lifton, B Boisson, L Abel, D Bogunovic, N Marr… - Nature medicine, 2021 - nature.com
The pathophysiology of adverse events following programmed cell death protein 1 (PD-1)
blockade, including tuberculosis (TB) and autoimmunity, remains poorly characterized. We …

[HTML][HTML] Life-threatening influenza pneumonitis in a child with inherited IRF9 deficiency

…, MJ Ciancanelli, L Abel, Q Zhang, N Marr… - Journal of Experimental …, 2018 - rupress.org
Life-threatening pulmonary influenza can be caused by inborn errors of type I and III IFN
immunity. We report a 5-yr-old child with severe pulmonary influenza at 2 yr. She is …

A recessive form of hyper-IgE syndrome by disruption of ZNF341-dependent STAT3 transcription and activity

…, M Bouaziz, T Habib, D Chaussabel, N Marr… - Science …, 2018 - science.org
Heterozygosity for human signal transducer and activator of transcription 3 (STAT3)
dominant-negative (DN) mutations underlies an autosomal dominant form of hyper–immunoglobulin …

Tuberculosis and impaired IL-23–dependent IFN-γ immunity in humans homozygous for a common TYK2 missense variant

…, B Fleckenstein, A Puel, MJ Ciancanelli, N Marr… - Science …, 2018 - science.org
Inherited IL-12Rβ1 and TYK2 deficiencies impair both IL-12– and IL-23–dependent IFN-γ
immunity and are rare monogenic causes of tuberculosis, each found in less than 1/600,000 …

Inherited IFNAR1 deficiency in otherwise healthy patients with adverse reaction to measles and yellow fever live vaccines

…, SJ Seligman, L Abel, P Hertzog, N Marr… - Journal of Experimental …, 2019 - rupress.org
Vaccination against measles, mumps, and rubella (MMR) and yellow fever (YF) with live
attenuated viruses can rarely cause life-threatening disease. Severe illness by MMR vaccines …

Encephalitis and poor neuronal death–mediated control of herpes simplex virus in human inherited RIPK3 deficiency

…, F Rozenberg, R Perez de Diego, RD Dix, N Marr… - Science …, 2023 - science.org
Inborn errors of TLR3-dependent type I IFN immunity in cortical neurons underlie forebrain
herpes simplex virus-1 (HSV-1) encephalitis (HSE) due to uncontrolled viral growth and …

[HTML][HTML] Inherited human IFN-γ deficiency underlies mycobacterial disease

…, CL Ku, Y Seeleuthner, V Béziat, N Marr… - The Journal of …, 2020 - Am Soc Clin Investig
Mendelian susceptibility to mycobacterial disease (MSMD) is characterized by a selective
predisposition to clinical disease caused by the Bacille Calmette-Guérin (BCG) vaccine and …